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Neuron-specific ablation of the Krabbe disease gene galactosylceramidase in mice results in neurodegeneration
Conlan Kreher
, Jacob Favret
, Nadav I. Weinstock
,
Malabika Maulik
, Xinying Hong
, Michael H. Gelb
, Lawrence Wrabetz
, M. Laura Feltri
, Daesung Shin
Research output
:
Contribution to journal
›
Article
›
peer-review
12
Scopus citations
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Dive into the research topics of 'Neuron-specific ablation of the Krabbe disease gene galactosylceramidase in mice results in neurodegeneration'. Together they form a unique fingerprint.
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Keyphrases
Ablation
100%
Axonal Degeneration
20%
Coordination Defects
20%
Demyelination
40%
Disease Genes
100%
Electron Microscopic Analysis
20%
Galactosylceramidase
100%
GalCer
60%
Gliosis
20%
Growth Coordination
20%
Krabbe Disease
100%
Motor Coordination
20%
Myelin
20%
Myelin Structure
20%
Myelinating Glia
20%
Nervous System
20%
Neurodegeneration
100%
Neuron-specific
100%
Neuronal Axon
20%
Neuronal Function
20%
Psychosine
40%
α-galactosylceramide (α-GalCer)
20%
Neuroscience
Axon
20%
Axonal Degeneration
20%
Galactosylceramidase
100%
Galactosylceramide
20%
Glia
20%
Gliosis
20%
Krabbe Disease
100%
Motor Coordination
20%
Myelin
40%
Nerve Fiber Degeneration
20%
Nervous System
20%
Neurodegeneration
100%
Psychosine
40%